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Facial Medial Dermoid Cyst -A Case Report

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An anterior facial medial dermoid cyst at the frontonasal suture in a 7-year-old male child is presented along with the images of computed tomography (CT) study. The CT scan images show clear nasal bone indentation with no erosion. Dermoid cysts are a subtype of benign heterotopic lesions termed choristomas and contain cutaneous elements which include squamous epithelium and dermal appendages such as hair, sebaceous glands, and sweat glands. Of all the pediatric head and neck dermoid cysts, periorbital cysts account for up to 9-10%. The periorbital dermoid may occur in two variants as per the plane of location: Anterior (superficial) or deep.
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ISSN (Online) : 2456-2688
Facial Medial Dermoid Cyst – A Case Report
Sajad Ahmad Salati*
Department of Surgery, Unaizah College of Medicine, Qassim University, KSA
Email: docsajad@gmail.com
Keywords: Choristoma, Medial Dermoid Cyst Congenital, Nasal Dermoid, Proptosis
Abstract
An anterior facial medial dermoid cyst at the frontonasal suture in a 7-year-old male child is presented along with the
images of computed tomography (CT) study. The CT scan images show clear nasal bone indentation with no erosion.
Dermoid cysts are a subtype of benign heterotopic lesions termed choristomas and contain cutaneous elements which
include squamous epithelium and dermal appendages such as hair, sebaceous glands, and sweat glands. Of all the pediatric
head and neck dermoid cysts, periorbital cysts account for up to 9–10%. The periorbital dermoid may occur in two variants

1. Introduction
Dermoid cysts are a subset of benign heterotopic
neoplastic lesions termed as choristomas. ey arise
from the epidermal rest cells that get pinched during
embryogenesis by the underlying developing bony
structures. In the pediatric population, the cysts in the
periorbital region account for about 10% of head and
neck dermoid cysts and generally occur in proximity
of frontonasal or frontozygomatic suture. e overall
prognosis of these lesions is good but they can rupture
and lead to severe inammation in the surrounding
tissues1,2. is report presents a case of an anterior facial
medial dermoid cyst in a 7-year-old male child.
2. Case Report
A 7-year-old male child, rst in the birth order, was
brought with a swelling at the bridge of the nose
(Figure1a-c). e parents had noted a fullness in the area
at the age of 9months and stated that the swelling had
progressively enlarged to become clearly noticeable. e
patient was born at full term by normal vaginal delivery
and had attained all the developmental milestones
normally. ere was no other signicant antenatal or
postnatal history. On examination, there was a single,
ovoid, non-tender, smooth, non-pulsatile, mobile, cystic,
subcutaneous lump about 2 cm × 1.5 cm located over the
right side of root of the nose, inferior to head of right
eyebrow, and superior to medial canthus. e lump
had minimal surface erythema and absent impulse on
coughing. Computed tomography (CT) scan imaging
shows a well-dened smooth margin fat-containing
extraconal mass located at the right side of root of the nose
with no intracranial extension. Bone window revealed
a clear indentation of right nasal bone but without any
bony erosion and the orbital anatomy was maintained.
ere were neither perilesional inammatory changes
nor any calcications.
e clinical presentation and imaging of the lesion
were most consistent with a medial dermoid cyst.
Excision of the cyst under general anesthesia was
planned and informed consent was secured from the
parents. e patient underwent an uneventful excision
of the cyst through a 2 cm long, transverse skin incision.
Histopathological study of the lesion demonstrated
a cystic structure lined with stratied squamous
keratinizing epithelium with skin adnexal structure
elements, consistent with a dermoid cyst. ere were no
postoperative complications. No recurrence was recorded
at 6 years follow-up and the parents were satised with
the outcome.
Journal of Health Science Research, Vol 6(1), 2021, 24-26
*Author for correspondence
How to cite this article: Salati SA. Facial Medial Dermoid Cyst – A Case Report. Journal of Health Science Research, 2021;6(1):24-26.
DOI: https://doi.org/10.7324/jhsr.2021.614
Facial Medial Dermoid Cyst – A Case Report
Vol 6 (1) | 2021 | https://jhsronline.com/index.php/jhsr Journal of Health Science Research
25
3. Discussion
Periorbital dermoid cysts are congenital and belong to a
subset of benign heterotopic neoplastic lesions termed
as choristomas1. ey are common in the pediatric
age-group and develop adjacent to the suture lines and
progressively enlarge as the child matures.
ese lesions are believed to evolve from the dermal
and the epidermal rest cells trapped during embryogenesis
in the cranial fusion lines as the closure of the neural tube
takes place2. Histologically, they have a lining of stratied
squamous epithelium with dermal adnexa such as hair
follicles, sebaceous, and sweat glands. e cyst contents
include keratin, hair, smooth muscle, and lipid debris3.
Dermoid cysts can be classied into (a) supercial or
anterior, and (b) deep varieties4.
Supercial dermoids, like the case presented in this
report, classically present as painless, rm, somewhat
mobile subcutaneous lumps. e lesions are usually
discovered by the parents/guardians in the 1st year
of their child’s life. With the growth of the child, the
periorbital facial fat normally decreases and this factor
results in making the cysts more prominent. Rarely the
supercial dermoid may rupture due to direct trauma,
extruding keratin and thence presenting with acute
inammatory features such as periocular erythema,
tenderness, and edema. Deeper orbital dermoids are
rare and grow indolently, presenting in the teenage or
even late adulthood with the gradual onset of globe
dystopia or proptosis and adjacent bony changes or
erosion5.
Anterior dermoid cysts most commonly occur at the
superolateral aspect of the orbit near the frontozygomatic
suture and less frequently are encountered as medial
lesions at the frontonasal suture as in case presented in
this report. Due to the anterior location, these lesions
usually do not result in globe displacement, but if proper
surgical attention is not sought and the lesion allowed
Figure 1. (a) External photograph (lateral view) demonstrates a mass on the right side of root of the nose, under the head of
the brow. (b) External photograph (anterior view) demonstrates a mass on right side of root of the nose, under the head of the
brow. (c) Immediate post-excision image with a sutured transverse incision. (d) Well-dened smooth margin low attenuating,
fat-density extraconal mass located on right side of root of the nose. (e) CT scan (bone window) showing clear indentation of
right nasal bone without any erosion.
d
c
b
a
e
Sajad Ahmad Salati
Vol 6 (1) | 2021 | https://jhsronline.com/index.php/jhsr Journal of Health Science Research 26
to grow to a large enough size, they have thesignicant
potential to cause visually signicant ptosis.
Imaging studies such as CT or magnetic resonance
imaging play an important role in determining the true
extent of the facial dermoid cysts and hence in planning
their appropriate management. Images should be obtained
for all the lesions not located in the superolateral quadrant
of the orbit and clinically suspected of being dermoid,
due to their tendency to grow stealthily deep into the
adjacent structures, creating a dumbbell shape. Imaging
is also indicated if the dermoid is nonmobile or presents
with features of inammation or stulization, and in the
presence of proptosis, globe dystopia, temporalis fossa
swelling, or optic neuropathy6.
e standard of care is complete surgical excision
without rupture of the cyst wall. e procedure is usually
straightforward for anterior cysts but deep orbital cysts may
present a surgical challenge requiring a dicult approach.
4. Conclusion
Periorbital dermoid cysts are congenital choristomas
that develop adjacent to the suture lines . Management
comprises of imaging studies to determine their extent
followed by complete surgical excision .
5. Acknowledgments
e author thanks the parents of the patient for sharing the
images and allowing their usage for academic purposes.
6. Authors’ Contributions
All the article has been draed by the author.
7. Financial Support and
Sponsorship
None.
8.  Conicts of Interest
None.
9. Ethics Approval and Consent
to Participate
Not applicable.
10.  Consent for Publication
Yes.
11.  References
1. Ahuja R, Azar NF. Orbital dermoids in children.
Semin Ophthalmol 2006;21(3):207-11. https://doi.
org/10.1080/08820530500353963. PMid: 16912019.
2. Yeola M, Joharapurkar SR, Bhole AM, Chawla M, Chopra S,
Paliwal A. Orbital oor dermoid: An unusual presentation.
Indian J Ophthalmol 2009;57(1):51-2. https://doi.
org/10.4103/0301-4738.44486. PMid: 19075411; PMCid:
PMC2661519.
3. Reissis D, Pfa MJ, Patel A, Steinbacher DM. Craniofacial
dermoid cysts: Histological analysis and inter-site
comparison. Yale J Biol Med 2014;87(3):349-57. PMid:
25191150; PMCid: PMC4144289.
4. Pham NS, Dublin AB, Strong EB. Dermoid cyst of
the orbit and frontal sinus: A case report. Skull Base
2010;20(4):275-8. https://doi.org/10.1055/s-0030-1247631.
PMid: 21311621; PMCid: PMC3023315.
5. Pryor SG, Lewis JE, Weaver AL, Orvidas LJ. Pediatric
dermoid cysts of the head and neck. Otolaryngol Head
Neck Surg 2005;132(6):938-42. https://doi.org/10.1016/j.
otohns.2005.03.005. PMid: 15944568.
6. Lin PH, Kitaguchi Y, Mupas-Uy J, Takahashi Y, Kakizaki H.
Rescue technique for complete removal of an accidentally
ruptured orbital dumbbell deep dermoid cyst: A case
report. Am J Ophthalmol Case Rep 2018;10:55-58. https://
doi.org/10.1016/j.ajoc.2018.01.044. PMid: 29780914;
PMCid: PMC5956660.
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Introduction: Dermoid cysts are common, benign, embryologically derived soft tissue cysts that can arise at a variety of craniofacial sites. It is not known whether specific histological variations exist between the different craniofacial sites. This study aims to establish whether inter-site histologic differences exist between periorbital, nasal, scalp, and postauricular dermoid cysts and analyze these in context of their distinct embryological origin and varied clinical presentation. Methods: A retrospective review of craniofacial dermoid cysts was performed. Using light microscopy with hematoxylin and eosin staining, histological appearance was directly compared between craniofacial sites. Results: All (n = 16) cysts contained keratinizing, stratified squamous epithelial lining, intraluminal keratin, and hair. Sebaceous glands were commonly present (n = 13). Eccrine (sweat) glands were less common (n = 3). Structures of mesodermal origin were seen in three periorbital cysts. Only the six ruptured cysts showed evidence of inflammation. Conclusions: Histological properties of dermoid cysts are conserved between craniofacial sites (periorbital, nasal, scalp, and postauricular). This reflects the consistency of ectodermal inclusion during early embryological development, which is independent of specific craniofacial site or surrounding anatomical structures.
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Dermoid cysts are developmental abnormal arrangement of tissues and are often evident soon after birth. Its occurrence in the orbit is relatively rare. We report a case of orbital floor dermoid in an 18-year-old female patient who presented with progressive, painless swelling in the lower eyelid associated with mild proptosis of three months duration. The lesion was excised completely, and histopathology confirmed the diagnosis of dermoid cyst.
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Purpose To report a rescue technique for complete removal of an accidentally ruptured orbital dumbbell deep dermoid cyst. Observations A 33-year-old female presented with left proptosis with retrobulbar discomfort for 3 months. Computed tomography images showed an orbital dumbbell deep dermoid cyst. A lateral orbitotomy was performed under general anesthesia. The cyst was ruptured during osteotomy of the lateral orbital rim. The cyst was opened vertically from the ruptured site using a Stephen's tenotomy scissors to visually confirm the internal wall of the cyst and to keep the epithelial lining intact while separating the external wall of the cyst from the bone. There was a small defect of the epithelial lining at the inferoposterior margin of the cyst. Granulomatous inflammation of the lacrimal gland was found adjacent to the defect site. The cyst was completely removed and the lacrimal inflammation subsided after the operation. Conclusions and importance Opening of the cyst is a useful technique to remove the entire epithelial lining of an accidentally ruptured dumbbell dermoid cyst.
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We describe a case of a dermoid cyst involving the orbit and frontal sinus of an adult treated at our tertiary referral center, and we review the literature on dermoid cysts of the orbit and frontal sinus. A 28-year-old Caucasian man presented with right-sided supraorbital swelling resulting in diplopia and reduced visual acuity. Computed tomography and magnetic resonance imaging scans were preformed. Although a definitive diagnosis was unclear, the imaging findings were consistent with a dermoid cyst. The lesion was excised through an upper-lid incision. Postoperatively, the patient had a patent frontal sinus and his visual symptoms resolved. Dermoid cysts of the orbit are uncommon lesions that occur primarily in the pediatric population. Lesions extending into the frontal sinus have not been reported before in the literature. In adults, orbital dermoids are more likely to present with bone erosion, and therefore they should be considered in the differential diagnosis for orbital and frontal bone lesions extending into the frontal sinus.
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To review the characteristics and determine treatment outcomes of pediatric dermoid cysts. Retrospective review of the presentation, diagnosis, treatment, and outcomes of all pediatric dermoid cysts of the head and neck examined between 1980 and 2002 at Mayo Clinic. Forty-nine patients (59% girls) had a dermoid cyst of the head and neck. The median age at diagnosis was 22 months. The most common presenting sign was a palpable mass, noted in 100% of patients. During evaluation, approximately 25 patients (51%) had imaging studies. The most common location of the cysts was periorbital (61%), followed by the neck (18%; including 1 submental cyst). Various surgical approaches were chosen. In 2 patients (4%), the dermoid cyst had an intracranial extension. Only 1 patient experienced recurrence. The median pathologic diameter of the cysts was 1.2 cm. Dermoid cysts are unusual neoplasms that often present in childhood, with the orbit being the area most commonly affected in the head and neck region. Imaging studies help rule out an intracranial or intraorbital extension. With complete excision, recurrence is unusual. Significance Our review will assist both primary care physicians and subspecialists in diagnosing and treating dermoid cysts.
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Orbital dermoid cysts are benign congenital choristomas. They are common in pediatric population, developing adjacent to suture lines, most commonly located in antero-lateral fronto-zygomatic suture, and are slowly progressive. Complete surgical excision without rupture of cyst is the standard of care. Deep orbital cysts cause proptosis, require imaging, and may present a surgical challenge with a difficult approach. Rupture of the cyst leads to severe inflammatory reaction in surrounding tissues. Overall prognosis remains good with isolated reports of malignancy masquerading as dermoid cysts.