Upon presentation, an erythematous patch on the neck and upper back.

Upon presentation, an erythematous patch on the neck and upper back.

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Patient: Male, 12 Final Diagnosis: Self-healing juvenile cutaneous mucinosis Symptoms: Facial edema • nodular skin lesion Medication: — Clinical Procedure: None Specialty: Pediatrics and Neonatology Objective Rare disease Background Self-healing juvenile cutaneous mucinosis (SHJCM) is a rarely diagnosed disease worldwide, with less than 20 report...

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Context 1
... closer inspection, the erythematous patch extended from the neck to the upper back (Figure 1) with no evidence of any papules, pustules, or vesicles. His palms and soles were com- pletely unremarkable. ...

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Article
Full-text available
Self-healing juvenile cutaneous mucinosis (SHJCM) is a rare childhood disease with characteristic cutaneous and rheumatic manifestations. Cutaneous manifestations include a combination of nodules affecting peri-articular (especially interphalangeal joints) and head and neck areas; and linearly arranged ivory white papules over an erythematous indurated skin. Despite a benign course, an abrupt onset of symptoms with extensive cutaneous involvement often leads to parental anxiety, overenthusiastic evaluation and sometimes aggressive treatment. A peculiar cutaneous distribution in SHJCM including nodular lesions and periorbital edema, arthritis and arthralgia in a few cases, may simulate juvenile dermatomyositis. It is, therefore, important for dermatologists and pediatricians to be aware of this entity. In this report, we describe two cases of SHJCM and briefly review similarly reported cases in children.