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Unilateral dermatomal venous malformation (VM). Digital subtraction angiography shows (A) normal vascular development of the brachial, radial, and ulnar arteries and (B) small peripheral VMs. C, Magnetic resonance angiography confirms this distribution pattern. D, Dermal VMs are strictly confined to the C6 dermatome.
Source publication
Venous malformations (VMs) are the most common vascular malformations, forming 44% to 64% of all vascular malformations. We report a case of a patient suffering from unilateral dermatomal VM. The VM was strictly confined to the right C6 dermatome. We propose that unilateral dermatomal VM is a prime example of somatic mosaicism in vascular developme...
Contexts in source publication
Context 1
... subtraction angiography showed normal anatomic development of the radial, ulnar, and interosseous arteries without any arteriovenous shunts (Fig 1, A). Direct injection of contrast substance into the largest VM of the thenar revealed irregular vascular cavities within the vein (Fig 1, B) and normal development of the major brachial veins. ...Context 2
... subtraction angiography showed normal anatomic development of the radial, ulnar, and interosseous arteries without any arteriovenous shunts (Fig 1, A). Direct injection of contrast substance into the largest VM of the thenar revealed irregular vascular cavities within the vein (Fig 1, B) and normal development of the major brachial veins. The venous tumors were confined to the subcutis and dermis of the dermatome C6 and did not infil- trate the muscles of the right hand and right forearm. ...Context 3
... were no visceral lesions and no enchondromas, underlining the general benign course of this disease. After magnetic resonance tomography of the right forearm (Fig 1, C), the tender, elastic nodules measuring 5 to 20 mm were once again surgically removed. Histopathologic eval- uation of the resected hemangiomas revealed well-circumscribed hypervascularized lesions consisting of dilated blood vessels with focal thrombi and slightly thickened vascular walls. ...Context 4
... eval- uation of the resected hemangiomas revealed well-circumscribed hypervascularized lesions consisting of dilated blood vessels with focal thrombi and slightly thickened vascular walls. The lesions were restricted to the C6 dermatome on the right forearm and have not recurred up to now on the right thenar, where dermis and subcutis had been radically resected and had been replaced by autologous skin transplantation from the left groin when the pa- tient was 35 years old (Fig 1, D). According to the Hamburg clas- sification of vascular malformations, this lesion is a venous, extratruncular, and limited malformation. ...