Figure 2 - uploaded by Mohamed Rahaoui
Content may be subject to copyright.
-Syndrome de Dandy-Walker : aspects en IRM foetale à 32 SA. a et b. Coupe sagittale mediane en ponderation T2. Noter l'insertion haute de la tente du cervelet (→), la dilatation du V4 ( * ) et l'agenesie du corps calleux (b). c. Coupe transversale en ponderation T2. Agenesie vermienne, dilatation du V4(*), avec refoulement à l'exterieur des deux hemispheres cerebelleux.
Source publication
Dandy-Walker syndrome (SDW) is a rare brain malformation that can be isolated or associated with other malformations. The diagnosis can be established in antenatal or postnatal, and the prognosis is related to the importance of the hydrocephalus and to frequent malformation associated.We propose, through these 3 observations, the contribution of ob...
Similar publications
Case Report Dandy-Walker syndrome is a heterogeneous group of cerebellar anomalies ranging from agenesis to hypoplasia or even early cerebellar atrophy. It can be isolated or associated with other malformations. The diagnosis can be made antenatal by morphological ultrasound in the second trimester or postnatal. The associated malformations and the...
Citations
... The Dandy-Walker malformation is frequently associated with other intracranial abnormalities such as agenesis of the corpus callosum found in our case. Also to be looked for: holoprosencephaly, occipital encephalocele and ocular anomalies [7][8][9]. Extra-cranial anomalies are also to be sought and are in order of frequency: cardiac anomalies (38%), facial dysmorphisms and cleft palate (26%), dysraphia, polyand syndactyly (28%), genito malformations -urinary (28%) and digestive (7%) [8]. ...
... Also to be looked for: holoprosencephaly, occipital encephalocele and ocular anomalies [7][8][9]. Extra-cranial anomalies are also to be sought and are in order of frequency: cardiac anomalies (38%), facial dysmorphisms and cleft palate (26%), dysraphia, polyand syndactyly (28%), genito malformations -urinary (28%) and digestive (7%) [8]. ...
... It not only helps to refine the diagnosis initially screened by ultrasound, but it can also represent a useful imaging technique for confirming and characterizing the various cerebellar malformations thanks to the median sagittal sections of the posterior fossa. At an early stage (19-24 weeks of gestation), it makes it possible to make the differential diagnosis between vermian malrotation and Dandy-Walker malformation by studying the biometry and morphology of all the structures involved [8]. ...
Case Report Dandy-Walker syndrome is a heterogeneous group of cerebellar anomalies ranging from agenesis to hypoplasia or even early cerebellar atrophy. It can be isolated or associated with other malformations. The diagnosis can be made antenatal by morphological ultrasound in the second trimester or postnatal. The associated malformations and the degree of hydrocephalus are the two essential criteria that condition the subsequent prognosis.We report a case series of three patients with Dandy Walker Malformation, including their clinical presentations, imaging findings, management, and outcomes. Additionally, we conducted a comprehensive literature review of Dandy Walker Malformations to provide a better understanding of the etiology, pathophysiology, diagnosis, and management of this condition.
... The Dandy-Walker malformation is frequently associated with other intracranial abnormalities such as agenesis of the corpus callosum found in our case. Also to be looked for: holoprosencephaly, occipital encephalocele and ocular anomalies [7][8][9]. Extra-cranial anomalies are also to be sought and are in order of frequency: cardiac anomalies (38%), facial dimorphisms and cleft palate (26%), dysgraphia, poly-and syndactyly (28%), genitor malformations -urinary (28%) and digestive (7%) [8]. other less common abnormalities include limb abnormalities, abdominal wall abnormalities and diaphragmatic hernia, which is extremely rare and found in our clinical case. ...
... Also to be looked for: holoprosencephaly, occipital encephalocele and ocular anomalies [7][8][9]. Extra-cranial anomalies are also to be sought and are in order of frequency: cardiac anomalies (38%), facial dimorphisms and cleft palate (26%), dysgraphia, poly-and syndactyly (28%), genitor malformations -urinary (28%) and digestive (7%) [8]. other less common abnormalities include limb abnormalities, abdominal wall abnormalities and diaphragmatic hernia, which is extremely rare and found in our clinical case. ...
... It not only helps to refine the diagnosis initially screened by ultrasound, but it can also represent a useful imaging technique for confirming and characterizing the various cerebellar malformations thanks to the median sagittal sections of the posterior fossa. At an early stage (19-24 weeks of gestation), it makes it possible to make the differential diagnosis between vermin malrotation and Dandy-Walker malformation by studying the biometry and morphology of all the structures involved [8]. Even in the second and third trimester, an inappropriate scan angle, can give the impression of excessive size of the cistern magna (great cistern) and even a vermin abnormality [14]. ...
Dandy-Walker syndrome is a heterogeneous group of cerebellar anomalies ranging from agenesis to hypoplasia or even early cerebellar atrophy. It can be isolated or associated with other malformations. The diagnosis can be made antenatal by morphological ultrasound in the second trimester or postnatal. The associated malformations and the degree of hydrocephalus are the two essential criteria that condition the subsequent prognosis. We report a case of Dandy-Walker malformation that was diagnosed during a first routine prenatal ultrasound at 17 weeks of gestation. We will detail the contribution of ultrasound in the diagnostic process by comparing it with the data in the literature. Obstetrics & Gynecology: Open Access Houssem R, et al. Gynecol Obstet Open Acc 7: 155. www.
