Figure 2- - uploaded by Ali Al Kaissi
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Sagittal MRI imaging revealing discontinuity of the cervical ligaments. Note the disruption of the anterior atlanto-occipital ligament, which connects the lower anterior clivus with the anterior aspect of the body of C2, as visualized by the superior continuation of the anterior longitudinal ligament. In addition, disruption of the anterior longitudinal ligament is evident (arrow-b). Note the dislocated atlas (arrow-c) and compression of the dura mater space. Line (d) represents the Wachenheim-clivus line (a method to evaluate craniocervical abnormalities). The line is drawn along the posterior aspect of the clivus, toward the odontoid process (OP). In normal subjects, the line is tangential to the posterior aspect of the OP. In contrast, in our patient, this line intersects the anterior aspect of the OP
Context in source publication
Context 1
... lateral craniocervical radiograph showed that, throughout the cervical spine, there was extensive fusion of both the anterior and posterior elements in association with occipito-vertebral dissociation (arrow) (Figure 1). MRI imaging revealed increased discontinuity/disruption of the ligaments effectively causing the observed occipito-vertebral dissociation (Figure 2). ...
Citations
Mobius Syndrome is a rare disorder characterized by congenital paralysis of the pair of nerves VI (abducens) and VII (facial), usually bilateral, which compromises the facial appearance, making it very expressive. Many are the commitments resulting from this syndrome that involve various orofacial disorders, including: bifid uvula, excessive salivation, micrognathia, absence of movement of the facial muscles, hypoplasia of the tongue, difficulty in closing the lips, facial asymmetry, absence of teeth, hard palate high arched, among others. Because of these characteristics, it is possible to observe changes in the speech of children with the syndrome. In light of that, this study aims to survey the publications indexed in international databases that contribute to characterize the speech of children with Mobius Syndrome. To that end, we have conducted a selection and analysis of studies that addressed the syndrome published between January 2008 and October 2013. We have found that there is a consensus, among the studies, regarding the impairment of communication, especially the speech of the subjects. But there are few studies that are concerned with characterizing the linguistic aspects of individuals with Mobius syndrome.
