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MRI of brain showing Chiari-II malformation with Hydrocephalus. Regions of Nepal Frequency(n) Percentage (%) Terai 57 58.8 Mountain 25 25.8 Himalaya 15 15.5
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p> Introduction: Neural tube defects are among the most common congenital malformations and a major cause of health problems in surviving children, especially in developing countries. Although the incidence of spinal dysraphism has significantly decreased over the last few decades, all over the world; however, the incidence is much higher in develo...
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... Per- centage (%) Other associated congenital anomalies were as tabulated in Table 4. Below is the picture (Figure 2) Total 9 cases were operated on emergency basis. Among those who were operated in emergency, 8 cases presented in state of ruptured and one case had gross hydrocephalus so anatomical repair and CSF diversion in the form of VP shunt was done in emergency. ...
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Congenital Myelomeningocele and congenital Hydrocephalus are among the most common pediatric neurosurgery diseases in Libya. This paper elucidates the experience of authors in clinical audit of seventy four cases diagnosed as congenital Myelomeningocele and hydrocephalus, in the period of time (Feb 2017 to Dec 2017). Materials and Methods: This was...
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... In a study byMetcalfe et al., 2006, post-operative improvement in 72% patients was reported. In the current study, 77% patients showed hydrocephalus(Kafle et al., 2017). The most common associated anomaly with spinal dysraphism is hydrocephalus.Kumar and Singh, 2003 ...
The development of the spinal cord can be summed up in three developmental stages: gastrulation (2–3 weeks), primary neurulation (3-4 weeks) and secondary neurulation (5–6 weeks). Any sort of deviance in any of these stages causes anomalies in spine and spinal cord; these anomalies are referred as spinal dysraphism. The approximated incidence of spinal dysraphism is about 1/1000 live births. The present study aims at varied presentations, management and surgical consequences in spinal dysraphism. Methods: A study on surgical treatment of spinal dysraphism was done over the period of 6 months from December 2019- May 2020 at GMC, Jammu. In the study at hand; the clinical aspects, management and surgical outcomes in case of spinal dysraphism were characterized. Results: A total of 30 patients of spinal dysraphism were operated with 70% males and 30% females. The age group selected for the study was between 0-3 years. In early post-operative period the most common symptoms were found to be meningitis (6%), minor wound infection (10%), major wound infections (14%) and 14% patients reported CSF leakage. Out of 30 patients who underwent surgery, 67% patients had good outcome, 20% reported satisfactory outcome and 13% reported poor outcome with an overall mortality rate of 13%. Conclusion: Spinal dysraphism is a complex disorder and requires a multidisciplinary approach for management. The present study suggests that surgery is the prominent treatment along with good post-operative care for the better life of the patient.
Tethered cord syndrome (TCS) encompasses a spectrum of congenital conditions that result in progressive neurological deterioration due to tension on the spinal cord and nerve root[1]. Patients with TCS present with a wide spectrum of symptoms hence detailed physical examination is vital in patients presenting with TCS. Although TCS is a well-known entity, it continues to pose challenges regarding diagnosis and management. Surgical untethering may either ameliorate these issues or halt their worsening if they have been long-standing for many years.
