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Rationale: Intraabdominal fibromatosis is a rare benign tumor that often affects the mesentery or retroperitoneum, and can infiltrate adjacent organs. However, it is rare for fibromatosis to arise from the small intestinal wall.
Patient concerns
A 27-year-old female with a tangible abdominal tumor is described.
Diagnoses
The computed tomography (...
Context in source publication
Context 1
... laparotomy, we found an 8-cm tumor in the horizontal section of the duodenum that was also connected to the ascending colon. The tumor was intact, and was not connected with intestinal mesenteries. Tumor mass resection, right colon resection, partial duodenum resection, and intestinal anastomosis were then performed. The gross pathology revealed that the tumor was intact, and almost the whole intestinal wall was invaded ( Fig. 2A and B). Pathological examination confirmed intestinal fibromatosis, showing proliferation of spindle cells and large amounts of collagen in the intracellular space (Fig. 3). The muscular layer of the intestinal wall was totally infiltrated, whereas the mucosa layer remained intact. Immunohistological examina- tion showed that the lesion was positive for actin and vimentin, but negative for CD34, CD117, S-100, and desmin. The patient recovered well and was discharged 1 week post- surgery. During 6 months of follow-up, the patient experi- enced no further ...
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Citations
... Intra-abdominal aggressive fibromatosis (desmoid tumor) is a locally aggressive tumor mostly originating from the retroperitoneal space or musculoaponeurotic tissues in the mesentery, showing fibroblast/myofibroblast proliferation, infiltrating adjacent tissues, and very rarely metastasizing to distant organs [1,2] . The most significant risk factors for intra-abdominal aggressive fibromatosis are positive family history, female gender, APC gene mutation, pregnancy, hormone therapy, and a history of surgical procedure and trauma. ...
... The most significant risk factors for intra-abdominal aggressive fibromatosis are positive family history, female gender, APC gene mutation, pregnancy, hormone therapy, and a history of surgical procedure and trauma. The tumor is mostly asymptomatic when it first emerges [1][2][3][4][5] . ...
... When it grows and starts to invade adjacent tissues or organs, however, it may produce signs and symptoms including abdominal discomfort, pain, palpable mass, intestinal obstruction, perforation, fistula, and inguinal hernia [1][2][3] . Depending on tumor size, growth pattern, and symptomatology, a staging model has been developed, which usually forms the basis for treatment planning [6] . ...
Mesenteric fibromatosis (MF) is a rare, locally aggressive tumor without distant metastasis, which has a high recurrence rate. Based on its location, it is classified as intra-abdominal, from abdominal wall, and extra-abdominal. The incidence of cystic-solid, retroperitoneal tumors is very low in comparison to other MF forms. Intra-abdominal MFs are asymptomatic in early stages, but their symptoms appear late in the tumor course. There is no specific imaging finding since radiological diagnosis is mostly impossible. Thus, diagnosis is made histopathologically. Nowadays, there is no consensus about its treatment although surgical resection is widely used. In the present study, a very rare case of cystic-solid retroperitoneal MF associated with separate synchronous skin tumors is reported.
