Figure 8 - uploaded by Arianna Di Stadio
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CT scan high-resolution images. (A) Type D CAA with preservation of the normal mastoid pneumatization. The red arrow indicates the squamosal suture. (B) Type D CAA with absence of mastoid pneumatization; the red arrow shows the clear presence of the squamosal suture that is still not closed.
Source publication
Auris atresia (AA) is a congenital pathology characterized by aplasia or hypopla-sia of the external ear with associated middle ear malformation. The AA has a different degree of severity, and the severe form of the disorder presents no identifiable ear canal (complete atresia) and absence or significative underdevelopment of the middle ear structu...
Citations
... As BAHI, we used a BAHA (R) applied with standard technique. 8 As CI, we used a Synchrony 2 by Medel; the CI electrode was inserted through the round window as illustrated in Figure 2. The patient did not present any complication after both surgeries. ...
We present a case of a 50-year patient with a severe form of otosclerosis (double ring) that was successfully implanted. We used a bone-anchored hearing implant for restoring the hearing in the right side and a cochlear implant in the left side; both surgeries did not show any complications. For reducing the risk of a secondary bone ossification related to the trauma of cochleostomy for electrode’s insertion, we used a round window approach. The patient recovered a normal auditory threshold and normal speech perception capacity both in silence and noise conditions 1 year after surgery.
... Patients with congenital atresia auris (AA) can have different types of deformities [5]; in some cases, patients present only with an external ear malformation [5] without bone alteration, while other patients have a severe malformation of the bone and the structures within the bone [6]. Patients with AA sometimes also have a modified course of the facial nerve or a prominent sigmoid sinus vein (SS) [5]. ...
... Patients with congenital atresia auris (AA) can have different types of deformities [5]; in some cases, patients present only with an external ear malformation [5] without bone alteration, while other patients have a severe malformation of the bone and the structures within the bone [6]. Patients with AA sometimes also have a modified course of the facial nerve or a prominent sigmoid sinus vein (SS) [5]. ...
... Patients with congenital atresia auris (AA) can have different types of deformities [5]; in some cases, patients present only with an external ear malformation [5] without bone alteration, while other patients have a severe malformation of the bone and the structures within the bone [6]. Patients with AA sometimes also have a modified course of the facial nerve or a prominent sigmoid sinus vein (SS) [5]. The malformation of one (or both) of these structures increases the intra-and post-operative risks even in simple procedures as BCI surgery [5]. ...
Purpose: Patients affected by severe atresia auris (AA) can present challenges during hearing restoration surgery due to the abnormal positions of vascular and nervous structures in the bone. A 3D reconstruction model of the malformed temporal bones can be helpful for planning surgery and optimizing intra- peri- and post-operative results.
Method: A 5-year-old girl with severe AA on the right side was implanted with a Bonebridge transcutaneous bone conduction implant (tBCI). 3D printing was used to reproduce the malformed temporal bone, find a good position for the tBCI and plan out the surgical details in advance. Hearing tests were performed before and after surgery and information about intra-, peri- and post-operative outcomes were collected.
Results: Thanks to the Bonebridge, the patient completely recovered hearing on the right side with no negative outcomes.
Conclusions: 3D printing is a useful tool for planning surgery in AA patients and for preventing possible risks related to the unknown malformed anatomy.
... Patients in group 3 were implanted with BAHA R 2 . The BAHA R was implanted percutaneously as previously described by Ricci et al. (2019) by the same surgeon with decades of experience in hearing devices. In this group, the BAHI was used as a CROS device. ...
Working memory (WM) function can be reduced in patients suffering from unilateral hearing loss (UHL) and can affect their academic performance. We aimed to compare the WM abilities of three categories of children with UHL: patients implanted with hearing aids (HAs), patients receiving a bone-anchored hearing implant (BAHI), and subjects who did not receive hearing devices. A randomized clinical study, in which 45 children (mean age: 9.5 years) were evaluated by pure tone audiometry (to identify the side and the severity of the UHL), was conducted in a tertiary referral center. Patients were simply randomized into three groups: (1) children without HAs (No-HA group), (2) patients with a (digital) HA (HA group), and (3) children with a BAHI (BAHI group). Their working and short-term memories were studied in both noisy and silent conditions at the recruiting time (T0, baseline) and 6 months after (T1) the treatment. Statistical analyses were performed to analyze the variances between T0 and T1 within each group and between the three groups. The No-HA group improved its T1 WM scores in silence (p < 0.01), but not in noise. The HA and BAHI groups showed statistically significant variances of T1 WM in noise (p < 0.01 and p < 0.01, respectively). The HA and BAHI groups did not show statistically significant variances compared to T1. Our results suggest that hearing devices (HA and BAHI) in children with sensorineural UHL (SUHL) can improve WM capacity in noise. We speculate that bilateral hearing capacity might improve the quality of life of this population, especially during everyday activities where noise is present.
