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Congenital cholesteatoma may be expected in abnormally developed ear, it may cause bony erosion of the middle ear cleft and extend to the infratemporal fossa. We present the first case of congenital cholesteatoma of the infratemporal fossa in a patient with congenital aural atresia that has been complicated with acute mastoiditis.
A sixteen year ol...
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Abstract
Introduction Canal wall down (CWD) mastoidectomy has many drawbacks, including chronic otorrhea not responding to medications, granulations, dizziness on exposure to cold or hot water, and tendency of debris accumulation in the mastoid cavity, demanding periodic cleaning. Many of these problems can be solved by re...
Hypothesis:
This study aimed to evaluate whether there is a difference in the degree of intracochlear trauma when the cochlear implant electrode arrays is inserted through different quadrants of the round window membrane.
Background:
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Citations
... Bilateral occurrence is more common than unilateral. 1 Schucknet 2 and other reported literature mention that 4 to 7% of cases of congenital EAC atresia also have congenital cholesteatoma, making it one of the rare diseases of the temporal bone. [2][3][4] The diagnosis of congenital cholesteatoma with canal atresia is very challenging. Imaging with DWI brain magnetic resonance imaging and temporal bone HRCT is helpful in confirming the diagnosis of cholesteatoma. ...
... Although rare, the incidence of congenital cholesteatoma is higher in ears with congenital aural atresia. 3 In this case, the patient has congenital cholesteatoma of the temporal bone. The disease described as congenital when it manifests itself without a past history of trauma or infection with intact and located behind the tympanic membrane. ...
... The disease described as congenital when it manifests itself without a past history of trauma or infection with intact and located behind the tympanic membrane. 3 Our case, presented with hearing loss, earache, facial paresis, postaural swelling after earache and had undergone incision and drainage, most likely he must have developed mastoiditis and mastoid abscess. Hidaka, et al. 4 had reported a case of congenital cholesteatoma of the mastoid region in a sixty-five years old man that presented with acute mastoiditis as the first presentation. ...
Congenital external canal atresia is one of the congenital ear anomalies that can occur in patients. Similarly, congenital cholesteatoma is also another congenital disease that is often diagnosed in early adulthood. Both the above-mentioned diseases can occur independently but the presence of both these entities is a rare occurrence and needs a high degree of suspicion aided by a computed tomography scan to make the diagnosis. We are presenting a case of a sixteen-year-old patient who presented with unilateral ear anomaly, earache, facial palsy, and postaural swelling and was diagnosed as a right sided congenital aural atresia with congenital cholesteatoma. He was surgically managed with right-sided modified radical mastoidectomy with canaloplasty and closure of mastoid fistula under general anesthesia.
... quadrant. [7] Levenson et al. in 1989 defined certain criteria for diagnosis of cholesteatoma of the middle ear including: (1) Presence of a whitish mass behind a normal TM, (2) a healthy pars flaccida and pars tensa, (3) no previous history of otorrhea or perforation, (4) No previous ear surgery, and (5) previous attacks of otitis media are not excluded. [8] In our case, no white mass appeared behind the TM. ...
Congenital cholesteatoma is defined as cholesteatoma occurring behind an intact tympanic membrane (TM). In the middle ear, it has different stages according to its site and relation with surrounding structures. We report an unusual case which is congenital cholesteatoma in the oval window and posterior mesotympanum surrounding a dehiscent fallopian canal in a young adult without obvious lesion behind intact TM, discussing its management. We have focused light in an unusual case in our practice and concluded that early intervention in such cases is recommended to prevent complications and planning a staged surgery is the treatment of choice.
... W 2012 r. Abdel-Aziz przedstawił przypadek 16-letniego chłopca z perlakiem wrodzonym kości skroniowej powikłanym zapaleniem wyrostka sutkowatego [37]. W tym samym roku Janardhan i wsp. ...
... Obserwacje kliniczne wykazały, że u chorych z perlakami wrodzonymi znacznie rzadziej niż z perlakami nabytymi dochodzi do powikłań wewnątrz-i zewnątrzskroniowych [13,33,37,38]. Fakt, że powikłania te rzadziej się obserwuje w perlakach wrodzonych niż nabytych, może wynikać z tego, że przy tak dużym zaawansowaniu, jakie jest konieczne do wystąpienia powikłania, błona bębenkowa jest zazwyczaj zniszczona i niemożliwe jest wówczas ustalenie etiologii perlaka. ...
... The aural atresia was a significant finding that is not reported in cases with Bezold's abscess and cholesteatoma. Although aural atresia was previously reported in cases with congenital cholesteatoma or children with cholesteatoma [9], it is only reported in one adult patient (a 30-year-old man) with an inflammatory granulation tissue and chronic osteomyelitis in the posterior part of the mastoid in CT scan [10]. In our patient, aural atresia and cholesteatoma was two risk factors that we could consider as leading causes for developing of a Bezold's abscess. ...
The Bezold’s abscess is an abscess in deep cervical spaces that is considered as
a complication of otomastoiditis. Antibiotics have produced an overall decline in
the frequency of complications of otitis media relative to the pre-antibiotic era.
Here we report a 23 year old male with Bezold’s abscess with unusual extension
to upper thorax.
Objective:
To conduct a retro- and prospective analysis of the clinical characteristics and results of surgical treatment of patients with congenital temporal bone cholesteatoma.
Patients and methods:
On the basis of the SPb Scientific Research Institute of ENT of the Ministry of Health of Russia 23 patients were diagnosed with congenital temporal bone cholesteatoma for the period from 2011 to 2018. There were 11 men (47.8%), 12 women (52.2%), the age of patients - from 2 to 44 years. The M.J. Levenson criteria were used to verify congenital middle ear cholesteatoma. (1986). According to intrasurgery findings, we identified congenital cholesteatoma of the middle ear stages according to the ChOLE classification. Other types of congenital temporal bone cholesteatoma included the patients with congenital atresia of the external auditory opening, combined with congenital temporal bone cholesteatoma; we found a patient with exostoses obstructing the external auditory canal combined with congenital cholesteatoma of the middle ear; and a patient with congenital cholesteatoma of the temporal bone pyramid.
Results:
An increase in the incidence of congenital temporal bone cholesteatoma was noted, which is probably due to increased awareness of specialists and the wider use of imaging research methods. A relationship was revealed between the stage of congenital cholesteatoma according to the ChOLE classification and the necessary volume of surgical intervention. Of the total number of cases of congenital temporal bone cholesteatoma, 26.1% were the patients with anomalies in the development of the outer and middle ear.
Conclusions:
All patients with suspected congenital temporal bone cholesteatoma require a temporal bone MSCT and middle ear MRI in DWI mode.
Hearing loss associated with craniofacial microsomia (CFM) requires a team approach for evaluation, diagnosis, aural rehabilitation, and surgical intervention. Age-appropriate hearing assessment is essential to appropriately diagnose associated hearing loss and provide early intervention services. Therapy is based on the anomalies associated with the craniofacial microsomia and can vary from ear-level hearing aids to bone conduction sound processors (BCSP), using either band or osseointegrated implant-retention systems to atresia repair. For many patients with favorable anatomy, aural atresia repair allows for improved conductive hearing and quality of life. In summary, unilateral hearing loss (UHL) should be treated early and appropriately to aid in optimal speech and language development, as well as age-appropriate school performance.
Objective:
Intracranial dermoid cysts are rare, slow-growing masses of sellar, parasellar regions, and posterior cranial fossa. The symptomatology of these cysts depends on the localization and presence of rupture. The preoperative diagnosis of these cysts by imagining techniques is distinctive as they have characteristic appearances.
Patient:
Endoscopic transnasal transpterygoid approach to infratemporal fossa for an extradural dermoid cyst of a 24 year-old woman is presented in this clinical report. Headache, dizziness, and retro orbital pain were her main complaints and diagnostic imagining studies designated an intracranial dermoid cyst preoperatively. The cyst was excised uneventfully with no recurrence 6 months after the operation.
Conclusion:
Surgery of intracranial lesions neighboring critical vital neurovascular structures can be challenging to the surgeon. Alternative minimal invasive approaches should always be considered for averting life-threatening complications.
Background:
Cholesteatomas are locally destructive collections of epithelial debris arising from temporal bone squamous epithelium. Recurrences may occur after removal and are typically located within the temporal bone.
Objective:
This study aimed to report a case of a massive, recurrent cholesteatoma with extension to temporoparietal scalp in a 37-year-old woman.
Methods:
Case report with literature review.
Results:
The patient underwent complete excision of a well-circumscribed left temporal mass, intraoperatively identified to arise from the middle ear and to contain keratin debris.
Conclusion:
We report a case of recurrent cholesteatoma with massive extension to temporoparietal scalp. Clinical suspicion of recurrent cholesteatoma should remain in the differential diagnosis of temporal mass with prior history of cholesteatoma.
