Fig 3 - uploaded by Nilda Espínola Zavaleta
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C. Vista interior de las cámaras derechas de un corazón con hipoplasia ventricular derecha, atresia pulmonar y septum ventricular íntegro. Obsérvese la posición del anillo anatómico de la VT (línea discontinua), la severa displasia de la VT (flecha) y un sinusoide miocárdico abierto (asterisco). Abreviaturas: VCS = Vena cava superior. CIA = Comunicación interatrial. Las demás abreviaturas iguales a las anteriores.
Source publication
In hypoplastic right ventricle the dysplasia of the tricuspid valve (TV) has repercussions on the development of the right ventricle. This paper documents the results of an anatomopathologic and morphometric studies of the tricuspid valve and the right ventricle in 25 hearts with this cardiopathy, which were morphologically analyzed using the segme...
Similar publications
In hypoplastic right ventricle the dysplasia of the tricuspid valve (TV) has repercussions on the development of the right ventricle. This paper documents the results of an anatomopathologic and morphometric studies of the tricuspid valve and the right ventricle in 25 hearts with this cardiopathy, which were morphologically analyzed using the segme...
Citations
El espectro del ventrículo derecho hipoplásico es amplio y desafiante, ya que dependiendo de su variabilidad anatómica y funcionalidad se planteará qué tratamiento es el adecuado. Presentamos el caso de un lactante de sexo femenino, de 15 meses de edad, quien cursó asintomática, valorada en consulta de seguimiento por cianosis con saturación de oxígeno del 70%, motivo por el cual es referida a nuestra institución.
Pulmonary atresia with intact ventricular septum is an apparently simple cyanotic congenital cardiopathy, characterized by several morphological variants and associated lesions leading to a complex diagnosis and treatment. The high mortality rate recorded in under 6 months-old infants demands an early aggressive management to face this situation. This review was intended to make a comprehensive assessment of the disease from its basic conceptual elements to the therapeutic variants to be adopted. To this end, the most important elements of morphology, physiopathology, diagnosis and treatment were addressed, in addition to discussing the roles of echocardiography, surgery and interventional cardiology techniques. The fundamental strategy of treatment is to separate the systemic circulation from the pulmonary circulation, causing neither reduction of the cardiac output nor increase of the central venous pressure. It is also aimed to return the right ventricle to the pulmonary circuit, provided that the coronary circulation does not depend on it. The algorithm presented in this paper underlined the importance of the integration of the surgical, interventional and hybrid modalities for the therapeutic management of this cardiopathy.
Introduction: pulmonary atresia with intact ventricular system is a cardiovascular malformation accounting for 1% of congenital cardiopathies seen in the extrauterine life; due to its unfavorable outcomes, this disease is a true challenge for the contemporary medicine. Objectives: the research study comprised the application of the classification guidelines, the characterization of the atresia outlet track, the morphological study of the right ventricle, the assessment of the tricuspid ring and the detection of anomalies in the coronary circulation. Methods: forty three patients diagnosed with this disease and referred to William Soler pediatric cardiocenter from January 1992 to November 2011 were studied. Each case was performed bidimensional echocardiography and color-coding Doppler. Results and conclusions: the study confirmed the predominance of the valvular morphological variant of the disease and the presence of moderate and severe levels of right ventricular hypoplexia associated with limited volumetric capacitance of this chamber, with tricuspid valvular hypodevelopment and with anomalous sinusoidsdependent coronary circulation. The permeable oral foramen was the interatrial septal defect that was most associated to this disease and several structural anomalies of the tricuspid system was evidenced in conjunction or not with the prevailing annular hypodevelopment.
