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A, B: Neutral position the sagittal T2-weighted MR image shows an unchanged spinal cord atrophy at the C4/5 to C6/7 vertebral body, without enlargement of the posterior epidural space. C-E: Unchanged anterior widening of the posterior epidural space about C3-C6/7 level (red arrows) with a few ow void signals inside on exion MR image sagittal T2-weighted image and contrast enhancement after supportive treatment after about 3 months.
Source publication
Hirayama’s disease, also known as juvenile non-progressive cervical amyotrophy or monomelic amyotrophy is a rare focal motor neuron disease that primarily affects young Asian males (15-25 years old). The À rst case was reported by Hirayama in 1959. The patient often has insidious and slowly progressive weakness, followed by a spontaneous arrest wit...
Contexts in source publication
Context 1
... diagnosis of Hirayama's disease was made at that time, based on typical clinical characteristics and classic MRI ndings on the exion position. Propranolol was prescribed for relieving tremors. At the three-month follow up, the tremors had signi cantly improved. The atrophy and weakness of his forearm and hands had not progressed. A repeated MRI study revealed an unchanged widening of the posterior epidural space in the exion position, with increased intensity enhanced after a Gadolinium injection ( Figure ...
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